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Hyperammonemia

1. N-Acetylglutamate synthetase deficiency

2. α-1-Antitrypsin deficiency

3. Argininemia

4. Argininosuccinic aciduria

5. Carbamoyl phosphate synthetase deficiency

6. Chemotherapy-induced hyperammonemia

7. Citrullinemia

8. Fatty acid oxidation disorders

9. HHH syndrome

10. HMG-CoA lyase deficiency

11. Isovaleric academia

12. Lysinuric protein intolerance

13. MCAD deficiency

14. Methylmalonic academia

15. Multiple carboxylase deficiency

16. Ornithine transcarbamylase deficiency

17. Pyruvate carboxylase deficiency

18. Pyruvate dehydrogenase complex deficiency

19. Propionic academia

20. Hyperthermia, malignant carnitine palmitoyl transferase-II deficiency

21. Transient hyperammonemia of the newborn

22. Urinary tract infection-urea slitting bacteria

23. Valproate

24. Wilson disease

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