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Hyperammonemia
1. N-Acetylglutamate synthetase deficiency
2. α-1-Antitrypsin deficiency
3. Argininemia
4. Argininosuccinic aciduria
5. Carbamoyl phosphate synthetase deficiency
6. Chemotherapy-induced hyperammonemia
7. Citrullinemia
8. Fatty acid oxidation disorders
9. HHH syndrome
10. HMG-CoA lyase deficiency
11. Isovaleric academia
12. Lysinuric protein intolerance
13. MCAD deficiency
14. Methylmalonic academia
15. Multiple carboxylase deficiency
16. Ornithine transcarbamylase deficiency
17. Pyruvate carboxylase deficiency
18. Pyruvate dehydrogenase complex deficiency
19. Propionic academia
20. Hyperthermia, malignant carnitine palmitoyl transferase-II deficiency
21. Transient hyperammonemia of the newborn
22. Urinary tract infection-urea slitting bacteria
23. Valproate
24. Wilson disease